Desmoplastic fibroma of the bone: Report of an unusual location with literature review

Abstract

Nihed Abdessayed, Ahlem Bdioui, Nozha Mhamdi, Marwa Guerfela, Moncef Mokni

Desmoplastic fibroma (DF) is an exceedingly rare benign primary tumor of bone, first described in 1958, which can be locally aggressive. It is considered to be the bony equivalent of the desmoid-type fibromatosis (aggressive fibromatosis of soft tissue). This tumor affects usually long bones and bones of the jaw; rib involvement is extremely uncommon. Its diagnosis is often challenging for the pathologist. Recognition of this entity is important to ensure proper surgical treatment. We report a case of DF of the rib in a 46-year-old woman, with lytic costal lesion and chest wall extension and we present a literature review of this rare disease.